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Rabbit Anti-MGAT4A/BF488 Conjugated antibody (bs-18907R-BF488)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價
產品編號 bs-18907R-BF488
英文名稱 Rabbit Anti-MGAT4A/BF488 Conjugated antibody
中文名稱 BF488標記的鈉/磷酸轉運蛋白1抗體
別    名 Alpha 1 3 mannosyl glycoprotein 4 beta N acetylglucosaminyltransferase A; Alpha 1 3 mannosyl glycoprotein beta 1 4 N acetylglucosaminyltransferase; GlcNAc T IVa; GNT IV; GNT IVA; MGT4A_HUMAN; GNTIV; GNTIVA; Mannosyl (alpha 1 3 ) glycoprotein beta 1 4 N acetylglucosaminyltransferase isoenzyme A; Mannosyl (alpha 1,3) glycoprotein beta 1,4 N acetylglucosaminyltransferase; MGAT 4A; N acetylglucosaminyltransferase IVa; N glycosyl oligosaccharide glycoprotein N acetylglucosaminyltransferase IVa; Na(+)/PI cotransporter 1; Na/Pi-4; Renal Na(+)-dependent phosphate cotransporter 1; Renal sodium-dependent phosphate transport protein 1; Sodium-dependent phosphate transport protein 1; Sodium/phosphate cotransporter 1; UDP GlcNAc:a 1 3 D mannoside b 1 4 acetylglucosaminyltransferase IV; UDP N acetylglucosamine: alpha 1 3 D mannoside beta 1 4 N acetylglucosaminyltransferase IVa; UDP N acetylglucosamine:alpha1 3 d mannoside beta1 4 N acetylglucosaminyltransferase  
規格價格 100ul/2980元 購買        大包裝/詢價
說 明 書 100ul  
研究領域 細胞生物  新陳代謝  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應 (predicted: Human, Mouse, Rat, Dog, Pig, Horse, Sheep, )
產品應用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 62kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human MGAT4A
亞    型 IgG
純化方法 affinity purified by Protein A
儲 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產品介紹 background:
MFSD8 is a 518 amino acid multi-pass membrane protein of the lysosome that is thought to function as a carrier protein that transports small solutes by way of chemiosmotic ion gradients. Expressed at low levels in many tissues, MFSD8 is encoded by a gene that maps to human chromosome 4q28.1. Defects in the gene encoding MFSD8 are the cause of a late infantile neuronal ceroid lipofuscinosis known as neuronal ceroid lipofuscinosis type 7 (CLN7). CLN7 is characterized by seizures, progressive dementia and visual failure.

Function:
May be a carrier that transport small solutes by using chemiosmotic ion gradients

Subcellular Location:
Alpha-1,3-mannosyl-glycoprotein 4-beta-N-acetylglucosaminyltransferase A soluble form: Secreted (By similarity).

Tissue Specificity:
Expressed at very low levels in all tissues tested.

Similarity:
Belongs to the glycosyltransferase 54 family.

Database links:

Entrez Gene: 6568 Human

Entrez Gene: 20504 Mouse

Entrez Gene: 171080 Rat

Omim: 182308 Human

SwissProt: Q14916 Human

SwissProt: Q61983 Mouse

SwissProt: Q62795 Rat

Unigene: 205816 Human

Unigene: 2656 Mouse

Unigene: 11150 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
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